USA USA / Tel: 1-631-624-4882    Europe Europe / Tel: 44-207-097-1828    Email Email:

Anti-GAA polyclonal antibody   (CPBT-35311RH)  


Rabbit anti-Human GAA (full length) polyclonal antibody for WB           Datasheet

  Add to basket
Specifications
Host Species
Rabbit
Antibody Isotype
IgG
Species Reactivity
Mouse, Human
Immunogen
Full length protein, corresponding to amino acids 1-952 of Human GAA.
Conjugate
Unconjugated
Applications
Application Notes
WB: 1/500 - 1/1000; IHC-P: 5μg/ml;

*Suggested working dilutions are given as a guide only. It is recommended that the user titrates the product for use in their own experiment using appropriate negative and positive controls.

Target
Alternative Names
GAA; glucosidase, alpha; acid; lysosomal alpha-glucosidase; glycogen storage disease type II; Pompe disease; 70 kDa lysosomal alpha-glucosidase; Acid alpha glucosidase; Acid maltase; Aglucosidase alfa; Alpha glucosidase; GAA; Glucosidase alpha acid (Pompe
Entrez Gene ID
2548
UniProt ID
P10253
Product Background
Pathway
Galactose metabolism, organism-specific biosystem; Galactose metabolism, conserved biosystem; Lysosome, organism-specific biosystem; Lysosome, conserved biosystem; Metabolic pathways, organism-specific biosystem; Notch-mediated HES/HEY network, organism-specific biosystem; Starch and sucrose metabolism, organism-specific biosystem; Starch and sucrose metabolism, conserved biosystem;
References
Liu, L; Dybvig, K; et al. GAA trinucleotide repeat region regulates M9/pMGA gene expression in Mycoplasma gallisepticum. INFECTION AND IMMUNITY 68:871-876(2000).
Franco, LM; Sun, BD; et al. Evasion of immune responses to introduced human acid alpha-glucosidase by liver-restricted expression in glycogen storage disease type II. MOLECULAR THERAPY 12:876-884(2005).
Custom Antibody Labeling
We offer labeled antibodies using our catalogue antibody products and a broad range of intensely fluorescent dyes and labels including HRP, biotin, ALP, Alexa Fluor® dyes, DyLight® Fluor dyes, R-phycoerythrin (R-PE), at scales from less than 100 μg up to 1 g of IgG antibody. Learn More

Online Inquiry

Please input "diagnostics" as verification code.
 Online Inquiry
Order Info:Anti-GAA polyclonal antibody
Interested in larger quantities ? request a quote!
Protocol may be improved. Please feel free to contact us to obtain the latest version.
15% off your first purchase

Contact Us

United States
Tel: 1-631-624-4882
Fax: 1-631-938-8221
Email:

Europe
Tel: 44-207-097-1828
Email:

Ordering Information

Payment methods we support:
✭ Invoice / Purchase Order
✭ Credit card
Credit card

Products
Antibodies
Antigens
Hybridomas
ELISA Kits
Rapid Test Kits
Materials and Reagents
Browse Key Words Alphabetically Hot
United States
Tel: 1-631-624-4882
Fax: 1-631-938-8221
Europe
Tel: 44-207-097-1828
Email

facebook   twitter   linkedin   google+
Distributors 

Home |  Copyright © 2009 - 2017 Creative Diagnostics. All rights reserved.
Inquiry Basket